Orthodontic and Orthognathic Management of a Patient with Osteogenesis Imperfecta and Dentinogenesis Imperfecta: A Case Report

Abstract

This case report describes a patient's severe Class III malocclusion, managed with a combination of orthodontic and orthognathic treatment. The medical history was complicated by osteogenesis imperfecta and dentinogenesis imperfecta. In addition the patient was a Jehovah's Witness.

Patients with osteogenesis imperfecta carry an increased risk of perioperative haemorrhage, and this led to bimaxillary surgery being carried out as two discrete surgical episodes for the patient described. In addition, the risk of enamel fracture led to orthodontic bands being cemented on all teeth. In spite of the increased risks a successful outcome was achieved.

Keywords

Orthognathic osteogenesis imperfecta

References

Kocher

, Shapiro

Osteogenesis imperfecta. [Review] J Am Acad Orthop Surg 1998; 6: 225–36.

O'Connell

. Marini JC. Evaluation of oral problems in an osteogenesis imperfecta population. Oral Surg Oral Med, Oral Pathol Oral Radiol Endod 1999; 87:189–96.

Schwartz

, Tsipouras

Oral findings in osteogenesis imperfecta. Oral Surg Oral Med, Oral Pathol Oral Radiol Endod 1984; 57: 161–7.

Ormiston

, Tideman

Orthognathic surgery in osteogenesis imperfecta: a case report with management considerations. J Craniomaxillofac Surg 1995; 23: 261–5.

Stenvik

, Larheim

, Storhaug

Incisor and jaw relationship in 27 persons with osteogenesis imperfecta. Scand J Dent Res 1985; 93: 56–60.