Multiple Bullae and Pulmonary Nodular Amyloidosis: A Rare Complication of Primary Sjögren's Syndrome

Abstract

We report the case of a 48 year-old woman with primary Sjögren's syndrome (pSS) who developed a rare but important pulmonary disorder associated with this condition. This case highlights the difficulty in making the diagnosis of this rare pulmonary disorder and the treatment challenges it poses.

Keywords

Pulmonary nodular amyloidosis Primary Sjögren's syndrome Cystic lung disease

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