An 8-year-old male presented with persistent left superior vena cava draining into the left atrium, hemizygous continuation, double outlet right ventricle, cor triatriatum, and visceroatrial discordance. After correction of the double outlet right ventricle and cor triatriatum at the age of 5, he developed mild cyanosis due to a persistent left superior vena cava draining into the left atrium. At the age of 8, an intraatrial tunnel was successfully constructed with bovine pericardium to reroute the abnormal systemic venous flow.
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